Search results for "Steroid 11-beta-Hydroxylase"

showing 7 items of 7 documents

21-Hydroxylase and 11beta-hydroxylase mutations in Romanian patients with classic congenital adrenal hyperplasia.

2005

Congenital adrenal hyperplasia (CAH) comprises autosomal recessive disorders mainly due to defects in the 21-hydroxylase (CYP21) gene.The study aimed to perform molecular characterization in 43 Romanian patients with classical CAH forms diagnosed at the Center for Genetic Diseases of the Pediatric Clinic/University Cluj (38 with 21-hydroxylase deficiency, five with 11beta-hydroxylase deficiency), to determine the frequency of mutations in the CYP21A2 gene and attempt a genotype-phenotype correlation in patients with 21-hydroxylase deficiency.Molecular analysis was performed by direct sequencing of PCR amplified products of the CYP21A2 and CYP11B1 genes.The most frequent mutation in Romanian…

AdultMalemedicine.medical_specialtyAdolescentGenotypeEndocrinology Diabetes and MetabolismClinical BiochemistryContext (language use)Biologymedicine.disease_causeBiochemistryEndocrinologyGene FrequencyInternal medicineGenotypemedicineHumansCongenital adrenal hyperplasiaSteroid 11-beta-hydroxylaseChildAllelesMutationAdrenal Hyperplasia CongenitalRomaniaBiochemistry (medical)Genetic disorder21-HydroxylaseInfantmedicine.diseaseEndocrinologyChild PreschoolMutationbiology.proteinMutation testingSteroid 11-beta-HydroxylaseFemaleSteroid 21-HydroxylaseThe Journal of clinical endocrinology and metabolism
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Aldosterone synthase activity in the Y-1 adrenal cell line.

1995

The Y-1 adrenal cell line was shown to produce 20 alpha-dihydroaldosterone from deoxycorticosterone. This compound was identified by GC-MS by comparison with the previously synthesized reference compound. Two other 18-hydroxylated metabolites were identified as 11 beta,18-dihydroxy-20 alpha-dihydroprogesterone from endogenous cholesterol and 18-hydroxy-20 alpha-dihydro-11-dehydrocorticosterone from DOC. The conditions necessary for the synthesis of these compounds are culturing in 20% serum-supplemented medium and repeated incubations with the substrate. The production of 11 beta-hydroxylated steroids and that of 18-oxygenated steroids is stimulated differently by ACTH and angiotensin II su…

Aldosterone synthasemedicine.medical_specialtymedicine.drug_classEndocrinology Diabetes and MetabolismClinical BiochemistryBiochemistryGas Chromatography-Mass SpectrometryCell LineMiceEndocrinologyAdrenocorticotropic HormoneCytochrome P-450 Enzyme SystemInternal medicineMineralocorticoidsmedicineAnimalsCytochrome P-450 CYP11B2RNA MessengerDesoxycorticosteroneMolecular BiologyGlucocorticoidschemistry.chemical_classificationbiologyAdrenal cortexAngiotensin IICytochrome P450Cell BiologyAngiotensin IIEnzymeEndocrinologymedicine.anatomical_structurechemistryBiochemistryCell cultureMineralocorticoidbiology.proteinAdrenal CortexMolecular MedicineSteroid 11-beta-HydroxylaseGlucocorticoidmedicine.drugThe Journal of steroid biochemistry and molecular biology
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Mapping of phenytoin-inducible cytochrome P450 immunoreactivity in the mouse central nervous system

1991

Abstract The distribution of phenytoin-inducible cytochrome P450 in non-treated mouse brain and spinal cord was analysed immunohistochemically using polyclonal antibodies against phenytoin-induced mouse cerebral microsomal P450. This P450 protein was proved in Ouchterlony [Volk B. et al. (1988) Neurosci. Lett. 84 , 219–224], Western blot, and immunohistochemical analyses to be reactive to the specific antibodies and an IgG fraction raised against phenobarbital-induced rat liver microsomal P450IIB1. The phenytoin-induced P450 is designated P450IIB1 * because immunologically it is comparable with P450IIB1; however, it has not yet been analysed for other characteristics of this enzyme. Immunoc…

Central Nervous SystemMaleCerebellumPathologymedicine.medical_specialtyCentral nervous systemPyramidal TractsBiologyMiceCerebellummedicineNeuropilAnimalsNeuronsGeneral NeurosciencePontine nucleiSpinal cordImmunohistochemistryPonsMice Inbred C57BLmedicine.anatomical_structurenervous systemEnzyme InductionPhenytoinSteroid 11-beta-HydroxylaseElectrophoresis Polyacrylamide GelBrainstemEpendymaNeuroscience
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Androgen hydroxylation catalysed by a cell line (SD1) that stably expresses rat hepatic cytochrome P-450 PB-4 (IIB1).

1989

Androgen hydroxylation catalysed by Chinese hamster fibroblast SD1 cells, which stably express cytochrome P-450 form PB-4, the rat P450IIB1 gene product, was assessed and compared to that catalysed by purified cytochrome P-450 PB-4 isolated from rat liver. SD1 cell homogenates catalysed the NADPH-dependent hydroxylation of androstenedione and testosterone with a regioselectivity very similar to that purified by P-450 PB-4 (16 beta-hydroxylation/16 alpha-hydroxylation = 6.0-6.8 for androstenedione; 16 beta/16 alpha = 0.9 for testosterone). Homogenates prepared from the parental cell line V79, which does not express detectable levels of P-450 PB-4 or any other cytochrome P-450, exhibited no a…

HemeproteinCytochromemedicine.drug_classBiologyHydroxylationBiochemistryCatalysisCell LineHydroxylationchemistry.chemical_compoundCricetulusCricetinaemedicineAnimalsTestosteroneAndrostenedioneMolecular BiologyAndrostenedioneCytochrome P450Cell BiologyFibroblastsAndrogenRatsBiochemistrychemistryLiverSteroid 16-alpha-HydroxylaseCell cultureSteroid HydroxylasesMicrosomebiology.proteinSteroid 11-beta-HydroxylaseAryl Hydrocarbon HydroxylasesResearch Article
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Identification and expression of the 11β‐steroid hydroxylase from Cochliobolus lunatus in Corynebacterium glutamicum

2019

Hydroxylation of steroids has acquired special relevance for the pharmaceutical industries. Particularly, the 11β-hydroxylation of steroids is a reaction of biotechnological importance currently carried out at industrial scale by the fungus Cochliobolus lunatus. In this work, we have identified the genes encoding the cytochrome CYP103168 and the reductase CPR64795 of C. lunatus responsible for the 11β-hydroxylase activity in this fungus, which is the key step for the preparative synthesis of cortisol in industry. A recombinant Corynebacterium glutamicum strain harbouring a plasmid expressing both genes forming a synthetic bacterial operon was able to 11β-hydroxylate several steroids as subs…

Operonlcsh:BiotechnologyGenetic VectorsGene ExpressionBioengineeringReductaseHydroxylationApplied Microbiology and BiotechnologyBiochemistryCorynebacterium glutamicumHydroxylation03 medical and health scienceschemistry.chemical_compoundPlasmidBiotransformationAscomycotalcsh:TP248.13-248.65Cloning MolecularResearch ArticlesBiotransformation030304 developmental biology0303 health sciencesbiology030306 microbiologyCochliobolus lunatusbiology.organism_classificationRecombinant ProteinsCorynebacterium glutamicumchemistryBiochemistrySteroid hydroxylaseSteroid 11-beta-HydroxylasebacteriaSteroidsBiotechnologyResearch ArticlePlasmidsMicrobial Biotechnology
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18-hydroxylation in the Y-1 adrenal cell line: response to ACTH and to culture conditions.

1992

The 18-hydroxylation of deoxycorticosterone in the Y-1 adrenal cell line was studied under various incubation and cell culture conditions and compared to 11 beta-hydroxylation. Repeated incubation of the substrate increased both 18- and 11 beta-hydroxylation in the Y-1 cells. Furthermore, both 18- and 11 beta-hydroxylation were increased with increased serum concentration and prolonged incubation time. While the increase in 11 beta-hydroxylation seemed to be independent of the type of serum, 18-hydroxylation was much more important in cells cultured in fetal or newborn calf serum supplemented medium than in those cultured in horse serum supplemented medium. As expected, ACTH treatment incre…

medicine.medical_specialtyCytochromeEndocrinology Diabetes and Metabolismmedicine.medical_treatmentClinical BiochemistryHydroxylationBiochemistryHydroxylationchemistry.chemical_compoundMiceEndocrinologyAdrenocorticotropic HormoneCytochrome P-450 Enzyme SystemInternal medicineAdrenal GlandsmedicineAnimalsCytochrome P-450 CYP11B2DesoxycorticosteroneMolecular BiologyIncubationCells CulturedFetusbiologyDose-Response Relationship DrugSubstrate (chemistry)Cell BiologyFetal BloodIn vitroCulture MediaSteroid hormoneEndocrinologyBloodchemistryCell cultureSteroid Hydroxylasesbiology.proteinMolecular MedicineSteroid 11-beta-HydroxylaseThe Journal of steroid biochemistry and molecular biology
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INHIBITION OF CELLULAR GROWTH AND STEROID 11β-HYDROXYLATION INRAS-TRANSFORMED ADRENOCORTICAL CELLS BY THE FUNGAL TOXINS BETICOLINS

1996

Abstract The proliferation of GM16 and 4CDTras-transformed newborn rat adrenocortical (RTAC) cells and Y1 mouse adrenal tumor cells was inhibited by beticolins, the fungal toxins extracted fromCercospora beticola, at submicromolar concentrations in a dose-dependent manner. Inhibitory concentrations for half the maximum inhibition were 150, 75 and 25 n M for beticolin-1 and 230, 150 and 50 n M for beticolin-2 in GM16, 4CDT and Y1 cells respectively. Beticolins strongly inhibited the production of 11β-hydroxysteroids on the second and third days of treatment in a dose-dependent manner between 0.1 and 1 μ M . Beticolins were shown by confocal microscopy to be localized in cytoplasmic organelle…

medicine.medical_treatmentAdrenal Gland NeoplasmsBiologyTransfectionHeterocyclic Compounds 4 or More RingsSteroidlaw.inventionHydroxylationMiceStructure-Activity Relationshipchemistry.chemical_compoundConfocal microscopylawOrganelleTumor Cells CulturedmedicineAnimalsCells CulturedHydroxysteroidsMicroscopy ConfocalDose-Response Relationship DrugCell growthCell BiologyGeneral MedicineMycotoxinsGrowth InhibitorsNeoplasm ProteinsRatsCell Transformation NeoplasticGenes rasAnimals NewbornchemistryBiochemistryCytoplasmAdrenal CortexSteroid 11-beta-HydroxylaseSignal transductionGrowth inhibitionCell DivisionCell Biology International
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